Case Report

Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature Review

Table 1

Hemodynamic parameters from right heart catheterization.

Hemodynamic parameters (units)Reference rangeCurrent PAH exacerbation

RAP (mmHg)2–6RAP 17/16
PAWP (mmHg)4–1214
PAP (mmHg)20–30 systolic97/52
8/12 diastolic
Mean PAP (mmHg)2569
CO (L/min)4–83.61
CI (L/min/m2)2.5–42.03
PVR (woods unit)0.5–1.115

RAP = right atrial pressure, PAWP = pulmonary artery wedge pressure, PAP = pulmonary artery pressure, CO = cardiac output, CI = cardiac index, PVR = pulmonary vascular resistance.