Clinical Study

Eosinophilic Cholangitis and Cholangiopathy: A Sheep in Wolves Clothing

Table 1

All reported cases of eosinophilic cholangitis.

CaseStudyGender age (yrs)Presenting symptomsEos.TreatmentStatus
AgeSex

1Rodgers et al., [2] 200150FAbdominal painNoRoux-en-Y, CENED, 2 mos
2Matsumoto et al., [3] 200738FAbdominal pain, jaundiceYesCSNED, 5 mos
3Vauthey et al., [4] 200344MAbdominal pain, jaundiceYesCSNED, 18 mos
4Duseja et al., [8] 200516FAbdominal pain, jaundiceYesCSNED, 12 mos
5Leegaard, [9] 198046MAbdominal pain, jaundiceNoCE, CSNED, 18 mos
6Rosengart et al., [10] 199048MAbdominal pain, jaundiceNoCENED, 5 mos
7Al-Abdulla et al., [11] 200042FAbdominal pain, jaundiceYesCE, CSNED
8Platt et al., [12] 199056FJaundice, ureteric obstructionNoCEN/A
9Schoonbroodt et al., [13] 199520MJaundice, feverYesCE, CSRecurred in stomach
10Grauer et al., [14] 199341MAbdominal pain, jaundice, feverYesCS, UrsodiolRecurred in kidney
11Jimenez-Saenz et al., [15] 200367FAbdominal pain, jaundiceYesCE, CSNED, 12 mos
12Butler et al., [16] 198532MAbdominal painYesCENED, 24 mos
13Tenner et al., [17] 199738FAbdominal painYesCE, CSNED, 3 mos
14Shanti et al., [18] 200133MAbdominal pain, jaundiceNoCE, hepatico-jejunostomyNED, 3 mos
15Shanti et al., [18] 200157FAbdominal pain, jaundiceNoRoux-en-YNED, 6 mos
16Song et al., [19] 199748FAbdominal painYesCE, T-tubeNED, 9 mos
17Scheurlen et al., [20] 199228MAbdominal pain, diarrheaYesHydroxureaNED
18Chen et al., [21] 200955MJaundiceYesRoux-en-Y, CE, CSNED, 9 mos
19Jeyamani et al., [22] 200713MFeverYesCSRecurred in liver
20Jeyamani et al., [22] 200726MFever, pruritisYesCSNED, 6 mos
21Sussman et al., [23] 200852MAbdominal pain, pruritisYesCS, AZT, UDCANED
22Raptou et al., [24] 200924MAbdominal pain, feverYesAspiration, AlbendazoleNED
23Current study, 200933MJaundice, pruritisNoRoux-en-Y, CE, portal lymph-adenectomy, common bile excisionNED, 13 mos

Note. Eos: Eosinophilia; CS: Corticosteroids; CE: Cholecystectomy; AZT: Azathioprine; UDCA: Ursodeoxycholic acid; N/A: Not available; NED: No evidence of disease.