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| S. number | Author | Year | Age (Y) | Gender | NF-1 | Clinical presentation | MRI/CT if MRI not available | Treatment approach | Path | Follow-up |
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| (1) | Lee et al. | 2016 | 49 | M | Yes | Asymptomatic, incidental findings of portal hypertension on EGD and US | Hypointense T1 lesion and low attenuating mass-like lesion with weak enhancement on T2 images | Medical management with beta-blockers for portal hypertension. Mass thought to be unresectable due to extension into hepatic hilum and lesser omentum | - | - |
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| (2) | Poon et al. | 2008 | 40 | M | No | 4-5-year history of intermittent upper abdominal pain with nausea and vomiting | T1 hypointense and in homogenously T2 hyperintense | Tumor resected en-bloc | Neurofibroma | 1 year |
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| (3) | Ghalib et al. | 1995 | 30 | F | Yes | Intermittent right upper quadrant pain | Low attenuating mass encasing the left portal vein, extending into the liver, extending into the gastrohepatic ligament, encasement of hepatic artery up to celiac axis | Exploratory laparotomy. Mass found to be unresectable | Plexiform neurofibroma | - |
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| (4) | Rastogi | 2008 | 35 | M | Yes | 6-month history of vague abdominal pain | Multiple hypoattenuating masses in the liver, porta hepatis, peripancreatic region and retroperitoneum | Nonsurgical management | - | 4 months |
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| (5) | Malagari et al. | 2001 | 24 | M | Yes | Asymptomatic, incidentally found on US | 7 cm well defined lesion in left hepatic lobe extending into porta hepatis and encasing the hepatic artery and celiac trunk | Exploratory laparotomy. Mass found to be unresectable | Plexiform neurofibroma | - |
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| (6) | Hoshimoto et al. | 2009 | 24 | F | Yes | Intermittent abdominal pain | T2 hyperintense tumor involving hepatoduodenal ligament and hepatic hilum, extending along intrahepatic Glisson’s sheath | The tumor was resected, leaving behind the intrahepatic extension | Plexiform neurofibroma | 3 years |
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| (7) | Ji et al. | 2017 | 54 | M | No | 3-month history of abdominal pain and weight loss of 3 months | 3.6 × 1.7 cm homogenous low-attenuation mass at the porta hepatis with irregular infiltrative margins, encasing and spreading along hepatic artery | Tumor resected; tumor was gradually peeled off from the hepatic artery along the arterial sheath | Plexiform neurofibroma | 18 months |
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| (8) | Gallego et al. | 1998 | 50 | M | Unknown | Unknown symptoms. Isolated neurofibromas in the liver, mediastinum, celiac axis and mesentery | Anomalous mesenteric and retroperitoneal tissue extending through hepatoduodenal ligament in to interhepatic periportal spaces. T1 hypointense and T2 hyperintense | Nonsurgical management | Plexiform neurofibroma | 2 years |
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| (9) | Rodríguez et al. | 1993 | 24 | M | Yes | Vague abdominal complaints | T1 hypointense and T2 hyperintense. Well defined mass around the porta hepatis and its peripheral branches. | Nonsurgical management | | 5 months |
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| (10) | Chen et al. | 1991 | 18 | M | Yes | Presented with PNF of the skull. Liver PNF incidental | Retroperitoneal neurofibroma with extension into the liver along the portal vein | Nonsurgical management | - | 3 months |
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