Research Article

Whole Body MRI at 3T with Quantitative Diffusion Weighted Imaging and Contrast-Enhanced Sequences for the Characterization of Peripheral Lesions in Patients with Neurofibromatosis Type 2 and Schwannomatosis

Table 1

Subject and lesion characteristics.

SubjectDiagnosisLesion diagnosisLesion locationLesion size (cm)T1w signalSTIR signalAverage ADC
(  mm2/sec)
Contrast-enhancement pattern

(1) NF-2PNSTChest2.2HypointenseHyperintense Homogeneous
PNSTAbdomen6.9HypointenseHyperintense Homogeneous
(2) NF-2PNSTPelvis1.2HypointenseHyperintense Homogeneous
PNSTPelvis1.0HypointenseHyperintense Homogeneous
(3)NF-2PNSTPelvis8.1HypointenseHyperintense Homogeneous
(4) NF-2CystParaspinal/L-spine2.2HypointenseHyperintense None
CystParaspinal/L-spine1.5HypointenseHyperintense None
PNSTT-spine2.6IsointenseHyperintense Homogeneous
PNSTThigh2.6IsointenseHyperintense Homogeneous
(5) NF-2PNSTChest2.2HypointenseHyperintense Homogeneous
PNSTChest2.8HypointenseHyperintense Homogeneous
(6) NF-2PNSTChest10.2HypointenseHyperintense Homogeneous
PNSTAbdomen6.4HypointenseHyperintense Homogeneous
PNSTArm3.5HypointenseHyperintense Homogeneous
PNSTThigh4.2HypointenseHyperintense Homogeneous
(7) SWNPNSTChest8.2IsointenseHyperintense Markedly heterogeneous
PNSTChest4.5IsointenseHyperintense Moderately heterogeneous
PNSTChest3.3IsointenseHyperintense Homogeneous
PNSTAbdomen8.2HypointenseHyperintense Moderately heterogeneous
PNSTAbdomen8.6HypointenseHyperintense Moderately heterogeneous
PNSTPelvis5.3HypointenseHyperintense Moderately heterogeneous
PNSTThigh8.1HypointenseHyperintense Moderately heterogeneous
PNSTThigh6.5HypointenseHyperintense Moderately heterogeneous
(8)NF-2No lesions
(9)NF-2No lesions
(10)NF-2No
Lesions
(11)NF-2No lesions

T1w: T1-weighted imaging; STIR: short tau inversion recovery.