Table of Contents
ISRN Dermatology
Volume 2013, Article ID 812029, 25 pages
http://dx.doi.org/10.1155/2013/812029
Review Article

Clinical Presentation, Pathogenesis, Diagnosis, and Treatment of Epidermolysis Bullosa Acquisita

Department of Dermatology, University of Lübeck, Ratzeburger Allee 160, 23538 Lübeck, Germany

Received 8 May 2013; Accepted 2 June 2013

Academic Editors: C. K. Janniger, F. Kaneko, E. Nagore, and E. Pasmatzi

Copyright © 2013 Ralf J. Ludwig. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Citations to this Article [42 citations]

The following is the list of published articles that have cited the current article.

  • Atsushi Shimizu, Artem Vorobyev, Hiroaki Iwata, Karsten Seeger, Katja Bieber, Navina Chrobok, Juergen Westermann, Rudolf Manz, Benjamin Tiburzy, Kathrin Kalies, Sarah Leineweber, Detlef Zillikens, Joerg Koehl, Ralf J. Ludwig, and Akira Ishiko, “B Cells, Dendritic Cells, and Macrophages Are Required To Induce an Autoreactive CD4 Helper T Cell Response in Experimental Epidermolysis Bullosa Acquisita,” Journal Of Immunology, vol. 191, no. 6, pp. 2978–2988, 2013. View at Publisher · View at Google Scholar
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  • Elvira Lazić-Mosler, Ines Lakoš Jukić, Slobodna Murat-Sušić, Karmela Husar, Mihael Skerlev, Zrinka Bukvić Mokos, Norito Ishii, Takashi Hashimoto, and Branka Marinović, “Inflammatory epidermolysis bullosa acquisita in a 4-year-old girl,” The Journal of Dermatology, 2015. View at Publisher · View at Google Scholar
  • Artem Vorobyev, Hideyuki Ujiie, Andreas Recke, Jacqueline J A Buijsrogge, Marcel F Jonkman, Hendri H Pas, Hiroaki Iwata, Takashi Hashimoto, Soo-Chan Kim, Jong Hoon Kim, Richard Groves, Unni Samavedam, Yask Gupta, Enno Schmidt, Detlef Zillikens, Hiroshi Shimizu, and Ralf J Ludwig, “Autoantibodies to Multiple Epitopes on the Non-Collagenous-1 Domain of Type VII Collagen Induce Blisters,” Journal of Investigative Dermatology, 2015. View at Publisher · View at Google Scholar
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  • Rolf Bambauer, Reinhard Latza, Daniel Burgard, and Ralf Schiel, “Therapeutic Apheresis in Hematologic, Autoimmune and Dermatologic Diseases With Immunologic Origin,” Therapeutic Apheresis and Dialysis, 2016. View at Publisher · View at Google Scholar
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  • Frida Dalin, Grazyna Adamus, Sufang Yang, Eva Landgren, Josefine Palle, Åsa Hallgren, Britt-Marie Frost, Therése Hugosson, Nils Landegren, Daniel Eriksson, Sten Andréasson, Khalid F. Tabbara, Olle Kämpe, and Mohammad Alimohammadi, “Aryl Hydrocarbon Receptor-Interacting Protein-Like 1 in Cancer-Associated Retinopathy,” Ophthalmology, 2016. View at Publisher · View at Google Scholar
  • Mareike Witte, Hiroshi Koga, Takashi Hashimoto, Ralf J. Ludwig, and Katja Bieber, “Discovering potential drug-targets for personalized treatment of autoimmune disorders – what we learn from epidermolysis bullosa acquisita,” Expert Opinion on Therapeutic Targets, pp. 1–14, 2016. View at Publisher · View at Google Scholar
  • Sidonia Mihai, Heike Albert, Ralf J. Ludwig, Hiroaki Iwata, Lars Björck, Mattias Collin, and Falk Nimmerjahn, “In vivo enzymatic modulation of IgG antibodies prevents immune complex-dependent skin injury,” Experimental Dermatology, 2016. View at Publisher · View at Google Scholar
  • L. Guerra, V. Pacifico, V. Calabresi, N. De Luca, D. Castiglia, C. Angelo, G. Zambruno, and G. Di Zenzo, “Childhood epidermolysis bullosa acquisita during squaric acid dibutyl ester immunotherapy for alopecia areata,” British Journal of Dermatology, 2016. View at Publisher · View at Google Scholar
  • Katja Bieber, Peter König, Jörg Köhl, Detlef Zillikens, Ralf J Ludwig, Mareike Witte, Shijie Sun, Jennifer E Hundt, Kathrin Kalies, Sören Dräger, Anika Kasprick, Trix Twelkmeyer, and Rudolf A Manz, “T cells mediate autoantibody-induced cutaneous inflammation and blistering in epidermolysis bullosa acquisita.,” Scientific reports, vol. 6, pp. 38357, 2016. View at Publisher · View at Google Scholar
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  • Ralf J. Ludwig, “Signalling and targeted therapy of inflammatory cells in epidermolysis bullosa acquisita,” Experimental Dermatology, 2017. View at Publisher · View at Google Scholar
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  • Philippe Bernard, and Frank Antonicelli, “Bullous Pemphigoid: A Review of its Diagnosis, Associations and Treatment,” American Journal of Clinical Dermatology, 2017. View at Publisher · View at Google Scholar
  • Stephen J. Challacombe, and Jane F. Setterfield, “Oral Vesicular and Bullous Lesions,” Contemporary Oral Medicine, pp. 1–60, 2017. View at Publisher · View at Google Scholar
  • Delphine Giusti, Sébastien Le Jan, Gregory Gatouillat, Philippe Bernard, Bach Nga Pham, and Frank Antonicelli, “Biomarkers related to bullous pemphigoid activity and outcome,” Experimental Dermatology, vol. 26, no. 12, pp. 1240–1247, 2017. View at Publisher · View at Google Scholar
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  • Seda Atay, Havva Hilal Ayvaz, and Müzeyyen Gönül, “Bullous Systemic Lupus Erythematosus and Cicatricial Pemphigoid,” Autoimmune Bullous Diseases, 2018. View at Publisher · View at Google Scholar
  • Delphine Giusti, Grégory Gatouillat, Sébastien Le Jan, Julie Plée, Philippe Bernard, Frank Antonicelli, and Bach-Nga Pham, “Anti-Type VII Collagen Antibodies Are Identified in a Subpopulation of Bullous Pemphigoid Patients With Relapse,” Frontiers in Immunology, vol. 9, 2018. View at Publisher · View at Google Scholar
  • Mareike Witte, Detlef Zillikens, and Enno Schmidt, “Diagnosis of Autoimmune Blistering Diseases,” Frontiers in Medicine, vol. 5, 2018. View at Publisher · View at Google Scholar
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  • Stephen J. Challacombe, and Jane F. Setterfield, “Oral Vesicular and Bullous Lesions,” Contemporary Oral Medicine, pp. 1083–1142, 2019. View at Publisher · View at Google Scholar
  • Hiroshi Koga, Catherine Prost-Squarcioni, Hiroaki Iwata, Marcel F. Jonkman, Ralf J. Ludwig, and Katja Bieber, “Epidermolysis Bullosa Acquisita: The 2019 Update,” Frontiers in Medicine, vol. 5, 2019. View at Publisher · View at Google Scholar