Case Report
Idiopathic Infantile Arterial Calcification: A Rare Cause of Sudden Unexpected Death in Childhood
Table 1
Long-term survivors with idiopathic infantile arterial calcification.
| Author | Age at diagnosis | Sex | Family history | Followup age/status | Cardiovascular findings | Treatment |
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Gleason et al. [2] | 5 years | M | No | 5 years/D | CHF | None | Gleason et al. [2] | 2 months | M | Yes | 5 years/A | NA | Steroid Thyroid estrogen | Gleason et al. [2] | Birth | F | Yes | 3 years/A | None | Diphosphonates | Gleason et al. [2] | 2 weeks | F | No | 7 years/A | Pulmonary stenosis | None | Gleason et al. [2] | 3 weeks | F | No | 22 years/A | Angina; myocardial infarction | Digoxin Disopyramide | Gleason et al. [2] | 10 days | M | No | 2 years/A | CHF, HT | Diphosphonates Digoxin | Gleason et al. [2] | Birth | M | Yes | 6 years/A | Arterial calcifications | Digoxin Diuretics | Rutsch et al. [3] | 5 days | M | Yes | 2,5 years/A | CHF | Antifailure Diphosphonates | Sebire and Sheppard [4] | 11 years | F | No | 11 years/D | CHF | Dobutamine | Patel et al. [5] | 2,5 years | F | No | 4,5 years/A | Headaches; failure to thrive | Anti-failure | van der Sluis et al. [6] | Birth | M | Yes | 25 years/A | None | Diphosphonates | Our case (2008) | 5 years | F | No | 5 years/D | CHF | None |
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CHF: cardiac heart failure; HT: hypertension; A: Alive; D: Dead; NA: nonavailable; Acute myocardial infarction.
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