Case Report

Idiopathic Infantile Arterial Calcification: A Rare Cause of Sudden Unexpected Death in Childhood

Table 1

Long-term survivors with idiopathic infantile arterial calcification.

AuthorAge at diagnosisSexFamily historyFollowup
age/status
Cardiovascular findingsTreatment

Gleason et al. [2]5 yearsMNo5 years/DCHFNone
Gleason et al. [2]2 monthsMYes5 years/ANASteroid
Thyroid estrogen
Gleason et al. [2]BirthFYes3 years/ANoneDiphosphonates
Gleason et al. [2]2 weeksFNo7 years/APulmonary stenosisNone
Gleason et al. [2]3 weeksFNo22 years/AAngina; myocardial infarctionDigoxin
Disopyramide
Gleason et al. [2]10 daysMNo2 years/ACHF, HTDiphosphonates
Digoxin
Gleason et al. [2]BirthMYes6 years/AArterial calcificationsDigoxin
Diuretics
Rutsch et al. [3]5 daysMYes2,5 years/ACHFAntifailure
Diphosphonates
Sebire and Sheppard [4]11 yearsFNo11 years/D CHFDobutamine
Patel et al. [5]2,5 yearsFNo4,5 years/AHeadaches; failure to thriveAnti-failure
van der Sluis et al. [6]BirthMYes25 years/ANoneDiphosphonates
Our case (2008)5 yearsFNo5 years/D CHFNone

CHF: cardiac heart failure; HT: hypertension; A: Alive; D: Dead; NA: nonavailable; Acute myocardial infarction.