Table of Contents Author Guidelines Submit a Manuscript
Sarcoma
Volume 1 (1997), Issue 2, Pages 109-111
http://dx.doi.org/10.1080/13577149778399
Case Report

Disseminating Adamantinoma of the Tibia

1Department of Surgery, Zuider-ziekenhuis Rotterdam, The Netherlands
2Department of Surgical Oncology, University Hospital Rotterdam/Dr Daniel den Hoed Cancer Center, Groene Hilledijk 301, EA Rotterdam NL-3075, The Netherlands
3Department of Orthopaedic Surgery, Academic Hospital Leiden, The Netherlands
4Department of Chest Disease, Zuider-ziekenhuis Rotterdam, The Netherlands

Copyright © 1997 Hindawi Publishing Corporation. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Patient. This report describes a patient with a primary long bone adamantinoma. The lesion was initially wrongly diagnosed as fibrous dysplasia and the patient was treated by curettage. At second local recurrence, the tumour had progressed from an osteofibrous dysplasia-like to a full-blown classic adamantinoma, with metastatic potential to the lungs 19 years after the initial treatment. Lung metastasectomy by sternotomy was carried out twice in a period of over 312 years. The patient is currently alive without evidence of other metastatic disease.

Discussion. From the files of the Netherlands Committee on Bone Tumors, another five patients with lung metastaseswere studied. All types of adamantinoma should be treated by complete en bloc resection. For patients with metastatic spread to the lungs, close radiological follow-up and excision of tumour nodules seems to be the only logic treatment modality.