Clinical Study

Survival in Malignant Peripheral Nerve Sheath Tumours: A Comparison between Sporadic and Neurofibromatosis Type 1-Associated Tumours

Table 1

Univariate analysis to determine factors significant for survival in patients without metastases at diagnosis.

FactorNF1SporadicAll patients
5 year survival (%)P5 year survival (%)P5 year survival (%)P

Stage1100100100
246.2.37576.1.07971.1.033

SiteLower limb55.669.466.7
Upper limb10083.390.9
Brachial plexus42.975.068.4
Sciatic plexus50.0.139100.03588.9.036

Volume 200 ml57.185.782.9
200 ml50.0.11966.7.01563.6.002

GradeLow44.474.270.0
High50.0.86279.2.71373.4.606

DepthSubcutaneous50.090.083.3
Deep50.0.37276.1.75572.2.571