Review Article

Targeting the p53 Pathway in Ewing Sarcoma

Table 4

Involvement of the EWS gene in translocation-based malignancies.

Tumour typeFusion geneTranslocationReference

Ewing SarcomaEWS-FLI1t(11;22)(q24;q12) [73]
EWS-ERGt(21;22)(q22;q12) [81]
EWS-ETV1t(7;22)(p22;q12) [82]
EWS-ETV4t(17;22)(q12;q12) [83]
EWS-FEVt(2;22)(q33;q12) [84]

Acute LeukemiaEWS-CIZ1t(12;22)(p13;q12) [85]

Angiomatoid Fibrous EWS-ATF1t(12;22)(q13;q12) [86]
HistiocytomaEWS-CREB1t(2;22)(q33;q12)[87]

Clear-cell SarcomaEWS-ATF1t(12;22)(q13;q12) [88]
EWS-CREB1t(2;22)(q33;q12) [89]

Desmoplastic Small Round Cell TumourEWS-WT1t(11;22)(p13;q12)[90]

Extraskeletal Myxoid EWS-CHN1t(9;22)(q22–31;q11-12)[91]
ChondrosarcomaEWS-NR4A3t(9;22)(q22;q12)[92]

Myxoid LiposarcomaEWS-DDIT3t(12;22)(q13;q12) [93]