Review Article

Multimodality Treatment in Ewing’s Sarcoma Family Tumors of the Maxilla and Maxillary Sinus: Review of the Literature

Table 2

ESFT, outcome as a function of treatment modality.

Chemo TX, aloneSurgery, aloneRadio(chemo)TX
(VAC, VCAD, VIDE)
no surgery
Radio(chemo)TX
(VAC, VCAD, VIDE)
plus surgery
Treatment not specified

PNET1 case [74]6 cases6 cases1 case
Ewing3 cases23 cases29 cases3 cases
Disease free upon follow-up ≥ 1 year1 case [92]12 cases15 cases1 case [68]
Max. follow-up4 months [74]26 months [92]23 years [52]>16 years [51]3 years [68]
Status upon max. follow-upDeadDisease freeDisease freeDisease freeDisease free