Clinical Study
Spectrum of Disorders Associated with Elevated Serum IgG4 Levels Encountered in Clinical Practice
Table 2
Spectrum of diagnoses associated with high serum IgG4 Levels (
).
| Diagnosis | No. of patients (%) |
| IgG4-related disease | 29 (18.4) | Definite | 10 | Probable | 0 | Possible | 19 | Respiratory diseases | 32 (20.3) | Bronchiectasis | 11 | Chronic rhinosinusitis | 7 | Asthma | 4 | Idiopathic pulmonary fibrosis | 3 | Sarcoidosis | 2 | Other respiratory diseases* | 5 | Biliary tract diseases | 26 (16.5) | Primary sclerosing cholangitis | 17 | Cholangiocarcinoma | 6 | Biliary stricture or stone | 3 | Pancreatic diseases | 19 (12.0) | Pancreatitis, not IgG4 related | 10 | Pancreatic cancer | 6 | Other pancreatic diseases† | 3 | Cirrhosis and other liver diseases | 9 (5.7) | Vasculitis | 9 (5.7) | Granulomatosis with polyangiitis (Wegener’s) | 5 | The Churg-Strauss syndrome | 3 | Polyarteritis nodosa | 1 | Atopic dermatitis | 1 (0.6) | Miscellaneous diseases‡ | 4 (2.5) | No specific diagnosis | 29 (18.4) |
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*Other respiratory diseases (5 patients) included chronic pleuritis, emphysema, fibrosing mediastinitis, hypersensitivity pneumonitis, and recurrent pneumonias, respectively. †Other pancreatic diseases (3 patients) included intraductal papillary mucinous neoplasm, pancreatic cyst, and pancreatic insufficiency, respectively. ‡Miscellaneous diseases (4 patients) included lactose intolerance, neurofibromatosis, polymyositis, and psoriasis, respectively.
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