Review Article

Behcet’s Disease: Is There Geographical Variation? A Review Far from the Silk Road

Table 3

The International Study Group criteria for Behcet’s Disease [16].

Recurrent oral ulcerationMinor or major aphthous, or herpetiform ulceration observed by physician or patient, which recurred at least 3 times in one 12-month period
Plus 2 of
Recurrent genital
ulceration
Aphthous ulceration or scaring, observed by the physician or patient
Eye lesionAnterior uveitis, posterior uveitis, or cells in vitreous on slit-lamp examination; or retinal vasculitis observed by an ophthalmologist
Skin lesionsErythema nodosum observed by the physician or patient, pseudofolliculitis, or papulopustular lesions; acneiform nodules observed by the physician in postadolescent patients not on corticosteroid treatment
Positive pathergy test Read by physician at 24–48 hours

(a) Findings applicable only in absence of other clinical explanations.