Behcet’s Disease: Is There Geographical Variation? A Review Far from the Silk Road
Table 3
The International Study Group criteria for Behcet’s Disease [16].
Recurrent oral ulceration
Minor or major aphthous, or herpetiform ulceration observed by physician or patient, which recurred at least 3 times in one 12-month period
Plus 2 of
Recurrent genital ulceration
Aphthous ulceration or scaring, observed by the physician or patient
Eye lesion
Anterior uveitis, posterior uveitis, or cells in vitreous on slit-lamp examination; or retinal vasculitis observed by an ophthalmologist
Skin lesions
Erythema nodosum observed by the physician or patient, pseudofolliculitis, or papulopustular lesions; acneiform nodules observed by the physician in postadolescent patients not on corticosteroid treatment
Positive pathergy test
Read by physician at 24–48 hours
(a) Findings applicable only in absence of other clinical explanations.