Review Article
Genetic and Clinical Features of Multiple Endocrine Neoplasia Types 1 and 2
Table 2
Prevalence of tumoral diseases in MEN 2 syndromes.
| Phenotype | MTC (%) | PHEO (%) | HPT (%) | Nonendocrinological associated pathologies (%) |
| MEN 2A | 95 | 50 | 25 | Cutaneous lichen amyloidosis (10%) | Hirschsprung’s disease (2%) | MEN 2B | 95 | 50 | | Mucosal neuromas (100%)
| Marfanoid habitus (100%) | Ganglioneuromatosis of the gastrointestinal tract (60%)
| FMTC | 100 | | | |
|
|