Table 1: Diseases and diagnostic criteria.

ANCA-associated vasculitides (AAV)

Microscopic polyangiitis (MPA)Chapel Hill Consensus Conference nomenclature [23]
Wegener’s granulomatosis (WG)ACR Classification Criteria for WG [24]
Churg-Strauss syndrome (CSS)ACR Classification Criteria for CSS [25]

Other vasculitides

Polyarteritis nodosa (PAN)ACR Classification Criteria for PAN [26]
Behçet’s disease (BD)International Criteria for BD [27]
Henoch-Schönlein purpura (HSP)ACR Classification Criteria for HSP [28]
Cryoglobulinemic vasculitisChapel Hill Consensus Conference nomenclature [23]
Secondary vasculitisDiagnostic criteria of underlying disease, histological confirmation
Undefined vasculitisClinical features without histological confirmation

Gastrointestinal disorders (GD)

Inflammatory bowel disease (IBD)Clinical, endoscopic, radiological and histological criteria [29]
Primary sclerosing cholangitisClinical, radiological and immunological criteria [30]
Autoimmune hepatitis (AIH)International Criteria for AIH [31]
Primary biliary cirrhosisClinical, biochemical, immunological and histological criteria [32]

Connective tissue diseases (CTD)

Systemic lupus erythematosus (SLE)Updated revised ACR Criteria for SLE [33]
Rheumatoid arthritis (RA)Revised ARA criteria for RA [34]
Felty’s syndromeClinical, radiological and laboratory criteria [35]
Systemic sclerosis (SSc)ARA preliminary classification Criteria for SSc [36]
Dermatomyositis (DM)Bohan and Peter diagnostic Criteria for DM [37, 38]
Sjögren’s syndrome (SjS)Revised International Classification Criteria for SjS [39]
Mixed connective tissue disease (MCTD)Alarcon-Segovia Diagnostic Criteria for MCTD [40]
Reiter’s syndromeClinical, radiological and immunological criteria [41]
Ankylosing spondylitisClinical, radiological and immunological criteria [42]
Juvenile chronic arthritisClinical, radiological and immunological criteria [43]
Relapsing polychondritisClinical, radiological and histological criteria [44]
PsoriasisClinical features
Antiphospholipid syndromeClinical and laboratory criteria [45]
Rheumatic polymyalgiaClinical features and laboratory findings


Tuberculosis (TBC)
S. aureus (subacute endocarditis)
Other bacterial infectionsClinical features and laboratory findings
Hepatitis C

Renal diseases (RD)

Poststreptococcal nephropathy (PSGN)
IgA nephropathyLaboratory and immunological findings, histological confirmation
Goodpasture’s disease
Membranous nephropathy


LymphomaClinical features, laboratory findings, histological confirmation
Chronic myelocytic leukaemia
Monoclonal gammopathies
Neurological disorders (ND)

Demyelinating disease
Neurological symptoms and imaging findings

Miscellaneous disorders

SarcoidosisClinical features, laboratory and imaging findings
Autoimmune hemolytic anemia (AHA)Clinical features and laboratory findings
Pulmonary fibrosisImaging findings, histological confirmation


Antithyroid drugs
AllopurinolHistory of medication treatment