Review Article

Genetic Counseling in Renal Masses

Table 3

Hereditary patterns and risks of renal cell carcinoma (RCC) associated syndromes.

SyndromeHereditary patternRisk of developing an RCC of the affected individuals

Von Hippel-LindauAutosomal dominant75%
Papillary RCCAutosomal dominant20%
Leiomyomatosis RCCAutosomal dominant10–16%
Birt-Hogg-DubéAutosomal dominant15–29%