Review Article
Genetic Counseling in Renal Masses
Table 3
Hereditary
patterns and risks of renal cell carcinoma (RCC) associated syndromes.
| Syndrome | Hereditary pattern | Risk of developing an RCC of the affected
individuals |
| Von Hippel-Lindau | Autosomal dominant | 75% | Papillary RCC | Autosomal dominant | 20% | Leiomyomatosis RCC | Autosomal dominant | 10–16% | Birt-Hogg-Dubé | Autosomal dominant | 15–29% |
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