Review Article

The Multifaceted Aspects of Interstitial Lung Disease in Rheumatoid Arthritis

Table 1

Histologic and clinical classification of IIPs, applicable to RA-ILD (adapted from [29ā€“31]).

Histologic patternsClinical-radiological-pathologic diagnosis

Usual interstitial pneumonia (UIP)(Idiopathic) pulmonary fibrosis/(cryptogenic) fibrosing alveolitis (IPF/CFA)
Nonspecific interstitial pneumonia (NSIP)Nonspecific interstitial pneumonia (NSIP)
Organizing pneumonia (OP)Organizing pneumonia (preferred definition) = Bronchiolitis obliterans organizing pneumonia (OP = BOOP)
Diffuse alveolar damage (DAD)Acute interstitial pneumonia (AIP)
Respiratory bronchiolitis (RB)Respiratory bronchiolitis interstitial lung disease (RB-ILD)
Desquamative interstitial pneumonia (DIP)Desquamative interstitial pneumonia (DIP)
Lymphoid interstitial pneumonia (LIP)Lymphoid interstitial pneumonia (LIP)