Cochlear Implant Outcomes and Genetic Mutations in Children with Ear and Brain Anomalies

Table 2

Demographic, clinical and audiological data and aetiologies of hearing loss.

	External ear malformations; (total = 3 cases)	Middle ear malformations; (total = 18 cases)	Inner ear malformations; (total = 30 cases)	Brain anomalies; (total = 119 cases)	Without brain anomalies; (total = 24 cases)
Sex (female : male)	1 : 2	9 : 9	11 : 19	55 : 64	9 : 15
Mean age (in years) at the time of surgery	3.0	3.0	4.4	4.0	7.0
Mean period (in months) of using cochlear implant	78	73	74	75	71
Implanted ear (°)	2L, 1R	8L, 7R, 3B	11L, 15R, 4B	42L, 61R, 16B	13L, 7R, 4B
% of progressive hearing loss	—	22.2%	30.0%	45.3%	54.1%
Cytomegalovirus infections	—	3	2	26	—
Meningitis	—	—	1	11	1
Genetic mutations	—	2	5	21	3
Syndromes	3	3	5	6	4
Unknown aetiology	—	3	—	26	1
Other conditions ()	—	2	2	19	1

(R = right; L = left; B = bilateral); (infant cerebral palsy, prematurity, perinatal suffering, hydrocephalus, ischemia, and neonatal icterus).