Cochlear Implant Outcomes and Genetic Mutations in Children with Ear and Brain Anomalies

Table 3

Anatomic distribution of inner ear malformations.

	Cochlear malformations; (total = 21 cases)	Vestibular and semicircular canal malformations (); (total = 24 cases)	Abnormal internal auditory canal (); (total = 15 cases)	EVA; ( = 21 cases)
Sex (female : male)	6 : 15	10 : 14	10 : 5	10 : 11
Mean age (in years) at the time of surgery	4	4	5	7
Mean period (in months) of using cochlear implant	75	77	84	54
Implanted ear (°)	8L, 11R, 2B	6L, 13R, 5B	7L, 8R	12L, 7R, 2B
Malformed side (°)	1L, 2R, 18B	1L, 2R, 21B	1R, 14B	1L, 3R, 17B
% of progressive hearing loss	28.6%	41.6%	26.6%	71.4%

(R = right; L = left; B = bilateral); (6 hypoplasias; 7 dilatations; 3 aplasias); (7 stenosis; 8 dilatations).