Cochlear Implant Outcomes and Genetic Mutations in Children with Ear and Brain Anomalies

Table 4

Types of cochlear malformations.

	Common cavity	Cochlear hypoplasia; (total = 6 cases)	Incomplete partition type 1; (total = 2 cases)	Incomplete partition type 2; (total = 7 cases)	Incomplete partition type 3; (total = 2 cases)	Cochlear basal turn dysplasia; (total = 4 cases)
Sex (female : male)	—	2 : 4	0 : 2	3 : 4	1 : 1	0 : 4
Mean age (in years) at the time of surgery	—	5	3	5	7	2
Mean period (in months) of using cochlear implant	—	59	82	85	77	73
Implanted ear (°)	—	2L, 4R	1L, 1R	2L, 4R, 1B	1L, 1R	2L, 1R, 2B
Malformed side (°)	—	1L, 1R, 4B	2B	1R, 6B	2B	4B
% of progressive hearing loss	—	40%	—	28.6%	50%	25%

(R = right; L = left; B = bilateral).