Research Article

Cochlear Implant Outcomes and Genetic Mutations in Children with Ear and Brain Anomalies

Table 5

Brain anomalies that were found among 143 implanted children.

Type of lesion/malformationTotal number of cases among 143 implanted children

Gliosis32
Dysmyelination/demyelination25
Leukomalacia24
Pineal cyst9
Arnold-Chiari malformation (type 1)7
Cerebellar hypoplasia 6
Cortical dysplasia5
Calcifications3
Arachnoid cyst3
(External) Hydrocephalus 3
Dilated lateral ventricles2
Corpus callosum hypoplasia2
Dilated fourth ventricle2
Trigonocephaly2
Facial nerve aplasia1
Pinealoma1
Hamartoma1
Hydrocephalus1
Bulbar atrophy 1
Cisternal dilatation1
Malignant neoplasm of encephalon (after surgery)1
Pellucid septum cyst1
Dilated subarachnoid space1
Focal ischemic lesions1
Microcephaly1
Lipoma1
(Occipital) Myelomeningocele1
Leukodystrophy1
Pachygyria1
Temporal lobe hypoplasia1