Cochlear Implant Outcomes and Genetic Mutations in Children with Ear and Brain Anomalies

Table 6

Different subgroups were defined to implement the statistical analysis.

Groups	Inclusion criteria	Number of cases
Main study group	Cochlear implant recipients who were less than 18 years of age at the time of surgery and who presented neuroradiological findings at preoperative neuroimaging investigations	143
Subgroup A	Patients with inner ear malformations (with or without brain anomalies)	23
Subgroup B	Patients with internal auditory canal stenosis	7
Subgroup C	Patients with only inner ear malformations (without brain anomalies)	13
Subgroup D	Patients with only brain anomalies (without inner ear malformations)	102
Subgroup E	Patients with inner ear malformations and brain lesions or abnormalities (with brain anomalies)	17
Subgroup F	Monolateral CI	123
Subgroup G	Bilateral CI	20
Subgroup H	<3 years of age at the time of surgery	61
Subgroup I	>3 years of age at the time of surgery	82
Subgroup J	Patients with genetic mutations	35
Subgroup K	Cytomegalovirus	26
Subgroup L	Meningitis (as the cause of the hearing loss)	13
Subgroup M	Patients who presented EVA	21
Subgroup N	CHARGE association	3
Subgroup O	Demyelination	25
Subgroup P	Gliosis	36
Subgroup Q	Leukomalacia	25
Subgroup R	Patient with only cochlear malformations	9