Research Article

Clinical and Laboratory Features of Acute Porphyria: A Study of 36 Subjects in a Chinese Tertiary Referral Center

Table 1

Clinical features and laboratory findings of acute porphyria.

Clinical manifestation ( = 36)

Abdominal pain32
Cyclical attacks28
Constipation26
Confusion16
Convulsions12
Tachycardia10
Paresis5
Numbness of extremities3
Hypertension3
Respiratory paralysis2

Laboratory findings

Hyponatremia29
Severe hyponatremia (<125 mEq/L)14
Serum Na (mEq/L)123.0 ± 10.7
Transaminase elevation22
ALT (U/L)69.5 ± 56.3
Anemia10
Hemoglobin (g/L)117.6 ± 17.9