Research Article

Skeletal Muscle Remodelling as a Function of Disease Progression in Amyotrophic Lateral Sclerosis

Table 1

Clinical characteristics of ALS patients included in the study.

Subject AgeDiagnosed Disease onsetAmbulationALSFRS-R
YearsYearsBL12 wk.BL12 wk.

168<1SpinalWalk uaWalk ua4241
247<1SpinalWalk uaWalk ww4038
365<1BulbarWalk uaWalk ua3836
46915SpinalWalk wbWalk wb3838
557<1SpinalWalk uaWalk ww4340

Ua: unassisted; wb: with ankle brace; ww: with walker. ALSFRS-R: ALS functional rating scale-revised.