Treatment and Patient Reported Outcome in Children with Hirschsprung Disease and Concomitant Congenital Heart Disease

Table 2

Summary of birth characteristics comparing children with Hirschsprung disease (HD) with and without congenital heart disease (CHD), presented as median (range) for birth weight and gestation age and as number (%) for gender, syndrome/chromosomal abnormality, cognitive disability within a syndrome, and congenital malformation. Pt = patients; = number.

Birth data	HD without CHD		HD and CHD		value
Birth weight (g)		3557 (2355–4675)	13	3344 (2100–4025)
Gestation age (weeks)		39.5 (32–42)		39.0 (36–42)
Gender (girls)	40	9 (23%)	13	3 (23%)
Syndrome or chromosomal abnormality (pt)	40	3 (8%)	13	9 (69%)
Cognitive disability (pt)	40	3 (8%)	13	3 (20%)
Congenital malformations (pt)	40	3 (8%)	13	2 (15%)
Number and types of malformations ()		3; External ear malformation; Congenital marmoreal telangiectasia cutis; Morgagni hernia		5; Hearing deficit Vertebral anomaly Brain asymmetry Alopecia; Ichtyosis

Information was missing in some of the children’s records.
Fisher’s exact test.
Mann–Whitney U test.