Treatment and Patient Reported Outcome in Children with Hirschsprung Disease and Concomitant Congenital Heart Disease
Table 5
Bowel function score (BFS) in children with Hirschsprung disease (HD) with and without congenital heart disease (CHD), median (range), aged 8 (4–10) and 6 (4–10) years, respectively, and the number of girls was 2 (33%) and 7 (27%), respectively. = numbers and (%).
Score
HD and CHD ()
HD without CHD ()
value
Ability to hold defecation
Always
3
0 (0%)
5 (19%)
Problems <1/week
2
1 (17%)
9 (35%)
Weekly problems
1
4 (67%)
11 (42%)
No voluntary control
0
1 (17%)
1 (4%)
Feels/reports the urge to defecate
Always
3
2 (33%)
5 (19%)
Most of the time
2
0 (0%)
13 (50%)
Uncertain
1
3 (50%)
6 (23%)
Absent
0
1 (17%)
2 (8%)
Frequency of defecation
Every other day to twice a day
2
2 (33%)
12 (46%)
More often
1
3 (50%)
11 (42%)
Less often
1
1 (17%)
3 (12%)
Soiling
Never
3
1 (17%)
0 (0%)
Staining <1/week
2
0 (0%)
13 (50%)
Frequent staining
1
2 (33%)
11 (42%)
Daily/requires protective aids
0
3 (50%)
2 (8%)
Fecal accidents
Never
3
2 (33%)
13 (50%)
Fewer <1/week
2
2 (33%)
7 (27%)
Weekly
1
0 (0%)
5 (19%)
Daily/requires protective aids
0
2 (33%)
1 (4%)
Constipation
No constipation
3
1 (17%)
19 (73%)
Manageable with diet
2
2 (33%)
4 (15%)
Manageable with laxatives
1
2 (33%)
2 (8%)
Manageable with enemas
0
1 (17%)
1 (4%)
Social problems
No social problems
3
3 (100%)
16 (67%)
Sometimes
2
0 (0%)
8 (33%)
Restricting social life
1
0 (0%)
0 (0%)
Severe social problems
0
0 (0%)
0 (0%)
Total BFS
Median 11 range (11–15)
Median 14 range (11–20)
2 and 3 patients in each group did not answer the question about social problems because of impaired cognitive disability which limited the answer rate in this question and also in total BFS. Fisher’s exact test. Mann–Whitney U test.
