Orthostatic Intolerance and Postural Orthostatic Tachycardia Syndrome in Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome, Hypermobility Type: Neurovegetative Dysregulation or Autonomic Failure?

Table 2

Valsalva maneuver in JHS/EDS-HT patients who performed the test (#22).

Variable	mmHg ± DS
Baseline SBP/DBP	116.7/73.9 ± 15.3/11.2
Maximal drop of SBP during early phase II	23.5 ± 9.96
Maximal drop of DBP during early phase II	4.8 ± 4.8
SBP at late phase II	125.9 ± 17.3
DBP at late phase II	85.4 ± 12.2
SBP at late phase IV	137.6 ± 21.2
DBP at late phase IV	84.0 ± 14.8
Difference between late phase II SBP and early phase II SBP	32.7 ± 15.6
Difference between late phase II DBP and early phase II DBP	17.6 ± 6.8

Normal values: Maximal drop of mean blood pressure (MBP) during early phase II: ≥20 mmHg; systolic blood pressure (SBP) and diastolic blood pressure (DBP) at late phase II: ≥baseline; SBP and DBP at late phase IV: ≥baseline.