Research Article

Orthostatic Intolerance and Postural Orthostatic Tachycardia Syndrome in Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome, Hypermobility Type: Neurovegetative Dysregulation or Autonomic Failure?

Table 5

Spectral parameters of heart rate variability and baroreflex sensitivity estimation.

JHS/EDS-HT ()Controls ()
RestTILTPRestTILTP
(rest versus tilt)(rest versus tilt)

Mean RR [s]0.91 ± 0.140.73 ± 0.12<0.0010.89 ± 0.100.76 ± 0.1<0.001
Tot power [msec2]3281 ± 28752187 ± 1423n.s2419 ± 14301961 ± 957n.s
LF power (u.n.)57.0 ± 21.782.7 ± 10.9<0.00157.5 ± 18.482.3 ± 14.6<0.001
HF power (u.n.)43.0 ± 21.717.3 ± 10.9<0.00142.5 ± 18.417.7 ± 14.6<0.001
LF/HF2.18 ± 1.998.36 ± 8.75<0.0011.98 ± 1.9612.0 ± 13.0<0.002
[msec/mmHg]59.1 ± 36.9++22.0 ± 9.6<0.00135.5 ± 11.018.5 ± 8.6<0.001
[msec/mmHg]21.6 ± 11.8+11.5 ± 5.8<0.00115.9 ± 5.810.8 ± 4.3<0.001
[msec/mmHg]37.5 ± 29.4++10.4 ± 5.2<0.00119.7 ± 7.87.7 ± 4.9<0.005

LF: low frequency
HF: high frequency
α: baroreflex sensitivity
JHS/EDS-HT versus controls; JHS/EDS-HT versus controls.