Research Article

Primary Cutaneous Lymphomas in Thailand: A 10-Year Retrospective Study

Table 4

Comparison of the frequencies of primary cutaneous lymphomas (PCLs) in different countries around the world.

AsiansCaucasians
Our studyJapanKorea (PCLs only)ChinaTaiwanIranUSA (PCLs only)Netherland + AustriaGermanySwitzerlandItaly
Author, YearPruksaeakanan et al., 2021Hamada et al., 2014, [8]Lee et al., 2016, [9]Shi et al., 2019, [10]Lee et al., 2018, [18]Naeini et al., 2015, [17]Bradford et al., 2009, [6]Willemze et al., 2005, [4]Assaf et al., 2007, [5]Jenni et al., 2011, [15]Maurelli et al., 2018, [3]
Study period2008-20172007-20112009-20132010-20182001-20102003-20132001-20051986-20021999-20041990-20092005-2015
Number of cases1371,73333385091993,8271,905998263141
Median age at diagnosis (yr)40654944.5NA36NANANA5664
Male : female1 : 1.41.3 : 11.6 : 1Male predominance1.6 : 11 : 1.21.4 : 1NANA1 : 1.41.8 : 1
CTCLs97.8%85.7%88.0%94.8%92.3%96.0%72.4%77.5%85.0%72.0%78.7%
Median age at diagnosis (yr)396447445036NANANA57.5NA
Mycosis fungoides67.9%43.3%49.0%65.4%57.1%86.9%38.9%48.0%62.0%43.0%50.3%
Sézary syndrome0.7%1.9%0%NA2.2%4.0%0.9%3.0%2.0%11.0%2.8%
ATLL0%16.7%0%NA0%NA0.1%NANANANA
pcCD30+ LPDs5.1%12.0%20.7%11.0%22.0%3.0%10.3%20.0%14.0%13.0%20.6%
pcALCL3.6%7.8%11.1%3.0%7.7%2.0%NA8.0%7.0%8.0%5.7%
LyP1.5%3.8%9.6%8.0%14.3%1.0%NA12.0%7.0%5.0%14.9%
SPTCL21.6%2.0%4.5%2.0%2.2%NA0.6%1.0%NANA0.7%
ENKTCL-NT0.7%2.0%5.4%5.0%4.4%1.0%0.3%<1%NA<1%0.7%
pcGDTCL1.5%0.3%1.8%NA0%NANA<1%NANANA
pcAECD8+ cytotoxic TCL0%0.3%0.6%NA0%NANA<1%NANANA
pcCD4+ small/medium T-cell LPD0%1.4%2.7%NA2.2%NANA2.0%5.0%3.0%2.8%
pcPTCL-NOS0.7%5.8%7.8%NA1.1%1.0%21.1%2.0%NA2.0%NA
CBCLs2.2%12.9%11.7%5.0%7.7%4.0%27.4%22.5%15.0%28.0%21.3%
Median age at diagnosis (yr)727056587840.5NANANA5365
pcMZL0%4.2%4.5%2.0%3.3%1.0%7.2%7.0%3.9%14%2.8%
pcFCL0.7%2.1%0.9%0.7%0%2.0%8.6%11.0%6.8%8.0%14.2%
pcDLBCL1.5%5.5%6.3%3.0%4.4%NA11.6%4.0%1.7%4.0%4.3%

CTCL: cutaneous T-cell lymphoma; pcCD30+ LPDs: primary cutaneous CD30+ lymphoproliferative disorders; pcALCL: primary cutaneous anaplastic large cell lymphoma; LyP: lymphomatoid papulosis; SPTCL: subcutaneous panniculitis-like T-cell lymphoma; ENKTCL-NT: extranodal NK/T-cell lymphoma, nasal type; pcGDTCL: primary cutaneous gamma/delta T-cell lymphoma; pcAECD8+ cytotoxic TCL: primary cutaneous aggressive epidermotropic CD8+ cytotoxic T-cell lymphoma; pcCD4+ small/medium T-cell LPD: primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder; pcPTCL-NOS: primary cutaneous peripheral T-cell lymphoma, not otherwise specified; CBCL: cutaneous B-cell lymphoma; pcMZL: primary cutaneous marginal zone lymphoma; pcFCL: primary cutaneous follicle center lymphoma; pcDLBCL: primary cutaneous diffuse large B-cell lymphoma; NA: not available.