IgG4-Related Sclerosing Cholangitis: Rarely Diagnosed, but not a Rare Disease

Table 3

Scoring system for the differentiation of IgG4-SC and PSC [73].

Variable	Category	Points
Other organ involvement	Yes	3
	No	0
Beaded appearance	Yes	0
	No	2
Age	<30 years	0
	30–39 years	1
	40–49 years	2
	50–59 years	3
	>60 years	4
Total score	Diagnosis
0–4	Probable PSC
5–6	Indicating diagnostic steroid trial
7–9	Probable IgG4-SC