Management of a Parturient with Mast Cell Activation Syndrome: An Anesthesiologist’s Experience

Table 1

Classification of disorders associated with mast cell activation.

PRIMARY	SECONDARY	IDIOPATHIC
(i) Clonal mast cell disorders (e.g., mastocytosis); (ii) Monoclonal mast cell activation syndrome	(i) Allergic disorders (e.g., asthma, rhinitis); (ii) Mast cell activation associated with inflammatory or neoplastic disorders; (iii) Physical urticaria; (iv) Chronic autoimmune urticaria	(i) Urticaria; (ii) Angioedema; (iii) Anaphylaxis; (iv) Mast cell activation syndrome(MCAS)

The term MCAS has been used interchangeably in the literature to denote both the umbrella term and idiopathic MCAS [4, 17].