Case Report
Myotonic Dystrophy and Anesthetic Challenges: A Case Report and Review
Table 2
Muscular impairment rating scale [
1].
| Grade | Description |
| Grade 1 | No muscular impairment |
| Grade 2 | Minimal signs: myotonia, facial weakness, jaw and temporal wasting, ptosis, no distal weakness except isolated digit flexor weakness |
| Grade 3 | Distal weakness, no proximal weakness except isolated elbow extensor weakness |
| Grade 4 | Mild to moderate proximal weakness |
| Grade 5 | Severe proximal weakness |
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