Case Report

Myotonic Dystrophy and Anesthetic Challenges: A Case Report and Review

Table 2

Muscular impairment rating scale [1].

GradeDescription

Grade 1No muscular impairment

Grade 2Minimal signs: myotonia, facial weakness, jaw and temporal wasting, ptosis, no distal weakness except isolated digit flexor weakness

Grade 3Distal weakness, no proximal weakness except isolated elbow extensor weakness

Grade 4Mild to moderate proximal weakness

Grade 5Severe proximal weakness