Case Report

Pulmonary Hemodynamic Changes with Nitric Oxide or Oxygen in a Patient with Asplenia, Single Right Ventricle, and Total Anomalous Pulmonary Venous Connection after Fontan Procedure

Table 1

Hemodynamic data in baseline.

SVC pressure (mmHg)15SVEF (%)67
IVC pressure (mmHg)15%SVEDV ()75
Conduit pressure (mmHg)15RsI (Um2)23.6
SVP (mmHg)105/e9RpI (Um2)2.1
rt PAP (mmHg)13Cardiac index (L⋅min−1⋅m−2)2.42
lt PAP (mmHg)13
rt lower PAWP (mmHg)8
lt lower PAWP (mmHg)7
AOP (mmHg)101/58 (72)

e: end-diastolic pressure; SVC: superior vena cava; IVC: inferior vena cava; SVP: single ventricle pressure; rt PAP: right pulmonary arterial pressure; lt PAP: left pulmonary arterial pressure; rt PAWP: right pulmonary arterial wedge pressure; lt PAWP: left pulmonary arterial wedge pressure; AOP: aortic pressure; SVEF: single ventricle ejection fraction; SVEDV: single-ventricle end-diastolic volume; : percent of normal; RsI: systemic resistance index; RpI: pulmonary resistance index.