Table of Contents Author Guidelines Submit a Manuscript
Case Reports in Cardiology
Volume 2018, Article ID 9025907, 3 pages
Case Report

Giant Right Atrial Aneurysm Accompanying Intrahepatic Cholestasis

1Department of Pediatric Cardiology, Gaziantep University Medical Faculty, Gaziantep, Turkey
2Department of Radiology, Gaziantep University Medical Faculty, Gaziantep, Turkey
3Department of Pediatric Gastroenterology, Kecioren Training and Research Hospital, Ankara, Turkey

Correspondence should be addressed to Ayse Sulu; moc.tenym@ulus_esya

Received 10 July 2017; Revised 18 October 2017; Accepted 23 October 2017; Published 28 February 2018

Academic Editor: Man-Hong Jim

Copyright © 2018 Ayse Sulu et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Right atrial aneurysms were first described in 1955, and subsequently, only a few cases have been reported. The etiology of this condition is unknown. Its comorbidity with cholestasis has not previously been reported in the literature. An 11-month-old baby female, who was an offspring from a first-cousin marriage, was referred to our hospital for investigation of jaundice. She underwent echocardiography because of a heart murmur, and this revealed a giant right atrial aneurysm. In addition, her liver biopsy confirmed the diagnosis of progressive familial intrahepatic cholestasis (PFIC) type 3. Although both conditions are rare, we found their comorbidity interesting and are thus reporting the case.