Case Report

Hyperammonemic Coma in an Adult due to Ornithine Transcarbamylase Deficiency

Figure 4

The urea cycle, demonstrating steps at which interventions are targeted in OTCD. ATP: adenosine triphosphate. ASAS: argininosuccinate synthetase. ASAL: argininosuccinate lyase. ARG-1: arginase 1.
493216.fig.004