Case Reports in Dentistry / 2021 / Article / Tab 1 / Case Report
A Case of Buccal Clear Cell Carcinoma Caused by Rare Fusion Gene: EWSR1-CREM Table 1 Clinical features and staining patterns of previously reported cheek or buccal mucosa CCC cases.
Authors Year Age Sex Size (cm) Metastasis Immunohistochemical staining Special staining Fusion type Treatment Recurrence Follow-up and outcome CK p63 CD10 S100 α -SMAKi-67 PAS d-PAS MC ALC Simpson et al. [14 ] 1990 66 M 2.5 — + NA NA — NA NA NA NA NA NA NA Sur — NED (11 y) Hiroki et al. [15 ] 1999 30 F 3 — + NA NA — NA NA + NA NA — NA Sur — NED Milchgrub et al. [16 ] 2000 29 F 2 +† NA NA NA NA NA NA NA NA NA NA NA Sur + REC (12 mo) O’Sullivan-Mejia et al. [17 ] 2009 78 F 1.7 — + — NA NA NA NA + NA — NA NA Sur — NED Solar et al. [9 ] 2009 49 F 3 NA + NA NA — — NA + — — NA NA Sur + REC × 2 (114 mo) Onoda et al. [11 ] 2012 59 F 0.8 — + — — — — NA + — NA — NA Sur — NED (4 y) Shah et al. [18 ] 2013 46 F NA +† + + NA — — NA NA NA NA NA EWSR1 re Rad, RS + NA 2013 37 F NA +† + + NA — — NA NA NA NA NA EWSR1 re Sur + NA Yamanishi et al. [3 ] 2015 52 F 1.5 — + + NA — — NA NA NA — NA EWSR1-ATF1 Sur — NED (11 y) Albergotti et al. [19 ] 2016 70 F 4.9 — NA NA NA NA NA NA NA NA NA NA EWSR1 re Sur — NED (13 mo) Hernandez-Prera et al. [20 ] 2017 57 F 2 — NA + NA — — NA NA NA — NA EWSR1-ATF1 Sur — NED (24 mo) Present study 2020 69 F 1.5 — + + — — — ± + — — — EWSR1-CREM Sur — NED (2 y)
NA: not available or not mentioned; NED: no evidence of disease; REC: recurrence; MC: mucicarmine; ALC: Alcian blue; re : rearrangement; Rad: radiotherapy; RS: reduction surgery; Sur: surgery. † Cervical lymph nodes.