Case Report

Chronic Periaortitis (Retroperitoneal Fibrosis) Concurrent with Recurrent Cutaneous Eosinophilic Vasculitis

Table 1

Compilation of the results of laboratory investigations at presentation.

Investigations with pathological results
 (i) Erythrocyte sedimentation rate: 107 mm/h
 (ii) C-reactive protein (CRP): 30.1 mg/L (normal: <6 mg/L)
 (iii) High sensitivity CRP: 27.0 mg/L (normal: <5 mg/L)
 (iv) Abdomen computed tomography (finding: chronic

Investigations with normal or negative results
 (i) Full blood count (including eosinophil count), lymphocyte
 subpopulation by flow cytometry of peripheral blood,
 hemoglobin, serum ferritin
 (ii) Serum: electrolytes (including Ca and PO4), fasting blood
 sugar, fasten lipids, urea, creatinine, uric acid, angiotensin
 converting enzyme (ACE)
 (iii) Liver and thyroid function tests
 (iv) Blood coagulation parameters, serum D-dimers
 (v) Urine chemistry and sediment
 (vi) Antinuclear antibody (ANA)1, extractable nuclear antigens
 (ENA), double-stranded DNA, antismooth muscle antibodies
 (ASMA), antimitochondrial antibodies (AMA), ANCA (-P, -C,
 -MPO and -PR3), anti-Ro/SSA, anti-La/SSB, rheumatoid
 factor,anticardiolipin antibodies (IgG and IgM)
 (vii) Complement levels; serum proteins electrophoretogram;
 serum immunoglobulins by immune electrophoretogram
 (including IgA and IgE)
 (viii) ASTO, RPR, serology for Borrelia burgdorferi,
Echinococcus, Toxocara canis, Hepatitis B and C viruses,
 Epstein-Barr virus and HIV
 (ix) Serological tumor markers (α-Fetoprotein (α-FP),
 carcinoembryonic antibody (CEA), Ca19.9, Ca15.3, Ca125)
 (x) Tuberculin skin test (TST = 2 mm)
 (xi) Schirmer’s test
 (xii) Chest imaging (X-ray and computed tomography)2

1Borderline positive (1 : 80, speckled pattern) at first examination; repeatedly negative (<1 : 80) on subsequent testing.
2Except for signs of chronic heart failure.