Case Report

Challenges in Management of Primary Hypoparathyroidism Associated with Autoimmune Polyglandular Syndrome Type 1

Table 1

Phenotypic manifestations of APS1 in affected family members.

PhenotypeII.1II.3II.4

Mucocutaneous candidiasis+++
Esophageal candidiasis++
Primary hypoparathyroidism+++
Primary adrenal insufficiency+++
Pernicious anaemia++
Vitiligo++
Type I diabetes mellitus++
Premature ovarian failure+++
Pancreatic exocrine insufficiency++