Case Report

SDHB-Associated Paraganglioma in a Pediatric Patient and Literature Review on Hereditary Pheochromocytoma-Paraganglioma Syndromes

Table 1

Work-up of suspected PCC/PGL.

Biochemical testing
 Fractionated urine metanephrines
 Fractionated plasma free metanephrines
 Chromogranin A

Anatomic imaging
 Ultrasound (children)
 CT
 MRI
Functional imaging
18F-Fluorodihydroxyphenylalanine PET
18F-Fluorodopamine PET
123I-MIBG single-positron emission CT