Case Report

Successful Management of Pheochromocytoma Detected in Pregnancy by Interval Adrenalectomy in a VHL Patient

Table 2


FeaturePregnancy induced hypertensionPheochromocytoma

HypertensionNot paroxysmalParoxysmal

Onset of hypertensionUsually after 20 weeks of gestationAny time during pregnancy

Other symptomsankle edema, proteinuria and an elevated plasma uric acid are commonankle edema, proteinuria and an elevated plasma uric acid are not common

Orthostatic hypotensionuncommonCommon

Syndromic features  
signs of NF1- café au lait spots, skin freckling or cutaneous fibromas
uncommonCan be seen