Two Portuguese Cochlear Implanted Dizygotic Twins: A Case Report

Table 1

Clinical history of the twins.

	ICC088 (III : 7)	ICC089 (III : 6)
Gender	Female	Male
Deafness etiology	Congenital	Congenital
Suspicion of deafness	18 months	18 months
Diagnosis	24 months	24 months
Clinical history	Normal pregnancy; No associated pathologies; No previous surgical procedures; 2 episodes of ear infections (otitis) prior implantation (without suppuration); No allergies; Vaccination plan up to date	Normal pregnancy; No associated pathologies; No previous surgical procedures; No allergies; Vaccination plan up to date
Audiogram	Neurosensorial bilateral profound deafness, stage 3	Neurosensorial bilateral profound deafness, stage 3
Placement of hearing aids	24 months	24 months
Gain with hearing aids	Very poor adaptation; No language development	Good adaptation; Functional gain up to 1000 Hz; No language development
Auditory evoked potentials (AEP)	Wave V present above 90 dB nHL on the right and above 100 dB nHL on the left	Absence of AEPs until 110 dB nHL bilaterally
Computerized axial tomography scan (CAT scan)	Morphologically normal and permeable cochlea; Normal inner ear canals	Morphologically normal and permeable cochlea; Normal inner ear canals
Magnetic resonance imaging (MRI)	No morphological alterations; No congenital malformations; No cochlear nerve atrophy; Normal cochleas	No morphological alterations; No congenital malformations; No cochlear nerve atrophy; Normal cochleas
Age at implantation	42 months	42 months
Duration of CI use	56 months	56 months
Age at audiological tests and present study	8 years	8 years
CI model	CI24R CA Advance	CI24R CA Advance
Speech processor	SPRINT	SPRINT
Stimulation mode	MP1+2	MP1+2
Stimulation strategy	ACE	ACE
Implanted ear	Right	Right