Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas

Table 1

Cases of pancreatic neoplasia in patients with dorsal agenesis of the pancreas.

Reference	Presenting symptoms	Imaging modality to confirm DAP	Operation	Final tumor histology
Matsusue et al. 1984 [3]	Abdominal pain, weight loss, hyperglycemia	ERCP	Total pancreatectomy	Ductal adenocarcinoma
Nakamura et al. 2001 [4]	None	ERCP	Subtotal pancreatectomy	Solid pseudopapillary tumor
Ulusan et al. 2005 [5]	Abdominal pain, type II diabetes mellitus	CT abdomen and pelvis	Pancreaticoduodenectomy	Solid pseudopapillary tumor
Ulusan et al. 2006 [6]	Abdominal pain, jaundice, hyperglycemia	Unknown	Hepaticojejunostomy	Ductal adenocarcinoma
Rittenhouse et al. 2011 [2]	Abdominal pain, type II diabetes mellitus	ERCP	Pancreaticoduodenectomy	Ductal adenocarcinoma
Rittenhouse et al. 2011 [2]	Abdominal pain, weight loss, type II diabetes mellitus	CT abdomen and pelvis	Pancreaticoduodenectomy	Ductal adenocarcinoma
Rittenhouse et al. 2011 [2]	Elevated liver function tests, asymptomatic	ERCP	Pancreaticoduodenectomy	Ductal adenocarcinoma
Kapoor and Singh 2011 [7]	Painless jaundice, weight loss, cholangitis	Intraoperative pancreatogram	Pancreaticoduodenectomy	Ampullary carcinoma
Sannappa et al. 2014 [8]	Jaundice, weight loss	MRI abdomen	Total pancreatectomy	Periampullary adenocarcinoma
Mistry et al. 2015 [9]	Painless jaundice, type II diabetes mellitus	CT abdomen and pelvis	Pancreaticoduodenectomy	Ampullary carcinoma