|
No. | Year | Sex | Age at onset | Age at treatment | Sites of lesions | Treatment | Outcome | follow up period from the 1st / last treatment (year) |
|
1 | 2001 [3] | F | 0 | 0 | — | right colectomy | — | 37 / — |
| 0–6 | — | partial gastrectomy, small bowel resection, total colectomy | blood transfusions required |
| 34–37 | small intestine, rectum | endoscopic sclerotherapy | oral iron, vitamin and caloric supplementation |
|
2 | 1996 [4] | F | 6 | 7 | intestine | surgical resection | stable for 5 years | 25 / 5 |
| 13 | small intestine, colon | surgical resection | stable for 5 years |
| 26 | duodenum, ileum, colon | surgical resection | stable for 5 years |
|
3 | 1997 [5] | M | 5 | 9 | stomach | endoscopic electrocautery | oral iron supplements and blood transfusions required | 21 / 1 |
| 23 | stomach, duodenum, small intestine, colon | intraoperative endoscopic polypectomy, surgical resection | stable for 1 year |
|
4 | 1990 [6] | F | 9 | 9 | whole GI tract | endoscopic sclerotherapy (for the upper and lower GI) | GI bleeding continued | 13 / short period |
| 15 | whole GI tract | surgical resection | stable for 4 years |
| 19 | upper and lower GI tract | intraoperative endoscopic electrocautery, surgical resection | stable for the short period |
|
5 | 2013 [7] | F | 1 | 12 | stomach | surgical resection | — | 13 / 3.5 |
| 22 | colon | endoscopic ligation and sclerotherapy | stable for 3.5 year |
|
6 | 2005 [8] | F | 19 | 19 | colon | endoscopic clipping | stable for 5 years | 7 / short period |
| 25 | small intestine, colon | endoscopic clipping and polypectomy, surgical resection | stable for the short period |
|
7 | 2009 [9] | M | 0 | 2 | stomach, colon | endoscopic electrocautery (for the stomach) | blood transfusions required for 4 years | 7 |
|
8 | 2003 [10] | F | 0 | 0 | colon | endoscopic APC | stable for 5 years | 5 |
|
9 | 2007 [11] | F | 8 | 12 | stomach, small intestine, colon | Surgical wedge resection, intraoperative endoscopic sclero-coagulation | stable for 5 years | 5 |
|
10 | 2010 [12] | M | 4 | 4 | stomach, colon | endoscopic sclerotherapy | — | 5 / 3 |
| 6 | small intestine | surgical resections through enterotomies | stable for 3 years |
|
11 | Our case | F | 4 | 5 | stomach, small intestine, colon | surgical resection | stable for 10 years with oral iron supplementation | 19 / 5 |
| 19 | stomach, duodenum, small intestine, colon | surgical resection, APC | stable for 5 year |
|