Case Report

Urachal Mucinous Cystic Tumor of Low Malignant Potential with Concurrent Sigmoid Colon Adenocarcinoma

Table 2

Summary of literature review of urachal mucinous tumors.

Primary Study AuthorYearNAgeSexPMPSize (cm)DiagnosisConcurrent neoplasmsPresentation/symptomsExtent of Surgical Treatment

Agrawal [16]2014150MYes8low grade mucinous urachal neoplasmNoAbdominal painCystic mass resection, partial cystectomy, extended parietal peritonectomy

Amin [10]20142424-80 (mean 47)9 M 
14 F 
1 UNK
Unk0.8-13 (mean 5)4 mucinous cystadenomas, 20 Mucinous cystic tumors of low malignant potentialNot mentioned, 1 case had a concurrent sigmoid colectomy performedHematuria, umbilical mass, incidental finding, suprapubic mass, mucusuria, abdominal pain, bladder dome nodule, urgency, obstruction, umbilical discharge, pelvic mass, midline cystic massCystic mass resection, partial cystectomy, umbilectomy

Carr [17]2001172MNo4Urachal mucinous tumor of uncertain malignant potentialNoHematuria (microscopic), nocturiaCystic mass resection, partial cystectomy

Chahal [18]2015137MNo4Mucinous cystic tumor of low malignant potential (MCTLMP)Yes - stage pT2, non-stem germ cell tumorIncidental findingPartial cystectomy, left hydrocelectomy

Choi [19]2012129FNo5.5Urachal mucinous tumor of uncertain malignant potentialNoRight flank painCystic mass resection, partial cystectomy

Fahed [20]2012166MNo9Adenocarcinoma in situNoLower abdominal pain and groin painCystic mass resection, partial cystectomy

Gupta [21]2014115FNo4.5Low grade mucinous neoplasm with uncertain malignant potentialNoLower abdominal painCystic mass resection

Hubens [22]1995140MNo8Urachal adenomaNoIncidental findingCystic mass resection, cholecystectomy

Hull [23]1994132MNo14Urachal CystadenomaNoIncidental findingCystic mass resection

Nozaki [24]2011137MYes5Mucinous borderline tumor of low malignant potentialNoAbdominal painCystic mass resection, extensive peritonectomy

Pasternak [25]2014128FNo8Mucinous urachal neoplasm of low malignant potentialNoIncidental findingCystic mass resection, partial cystectomy, umbilectomy, omentectomy, bilateral pelvic lymphadenectomy

Paul [26]1998168MNo3Stage 0 mucinous adenocarcinoma in situ of the urachusNoHematuria, mucusuriaCystic mass resection, partial cystectomy

Prakash [27]2014158MNo10Complex mucinous cystadenoma of undetermined malignant potential of the urachusNoLower abdominal painCystic mass resection

Saha [28]2011160FNo3Mucinous cystadenomaNoUrinary frequencyCystic mass resection

Schell [29]2009170FNo15.5Complex mucinous cystadenoma of undetermined malignant potential of the urachusNoLower abdominal massCystic mass resection, partial cystectomy

Shinohara [30]2006154MYes9Mucinous cystic tumour with low malignant potentialNoFound incidentally during left inguinal hernia repairCystic mass resection, partial cystectomy, intraperitoneal lavage

Stenhouse [31]2003154MYes14Mucinous neoplasm of uncertain malignant potentialNoAbdominal pain, rectal bleedingNot available

Wang [32]2016154MNo4Urachal mucinous cystic tumor of low malignant potentialNoHip painCystic mass resection, partial cystectomy, umbilectomy

Wu [33]2017141MNo3Urachal cystadenoma with unknown malignant potentialNoLower abdominal swelling and painCystic mass resection, partial cystectomy

PMP: pseudomyxoma peritonei; UNK: unknown.