Case Report

A Case of Acquired Haemophilia A in a Patient with Chronic Myelomonocytic Leukaemia

Table 1

Clinical data on admission.

Normal range

White blood cell13.6 × 109/L(3.5–9.7)
Neutrophil7.6 (56.1%) × 109/L(38–74%)
Eosinophil0.16 (1.2%) × 109/L(0–8.5%)
Basophil0.03 (0.2%) × 109/L(0–2.5%)
Monocyte4.6 (33.6%) × 109/L(2–10%)
Lymphocyte1.2 (8.9%) × 109/L(16–50%)
Red blood cell 312× 104/μL(400–550)
Haemoglobin8.8 g/dL(13.2–17.2)
Haematocrit28.1%(40–52)
MCV90.1%(85–103)
Platelet258 × 109/L(140–370)
AST18 IU/L(13–33)
ALT12 IU/L(8–42)
CK38 IU/L(62–287)
LD270 IU/L(119–229)
Total bilirubin0.93 mg/dL(0.2–1.3)
BUN15.0 mg/dL(8–20)
Creatinine0.77 mg/dL(0.6–1.1)
Total protein6.4 g/dL(6.7–8.3)
Albumin3.7 g/dL(3.9–4.9)
CRP2.37 mg/dL(<0.3)
PT13.7 s(10.5–14)
APTT85.8 s(24–39)
Fibrinogen458 mg/dL(200–400)
FDP5.6 μg/mL(<5)
Anticardiolipin β2GPI<1.2 U/mL(<3.5)
Anticardiolipin antibody<8 U/mL(<10)
Lupus anticoagulant1.06 ratio(<1.3)
Factor VIII activity<1%(60–150)
Factor IX activity34%(70–130)
Factor XI activity20%(75–145)
Factor XII activity19%(50–150)
Factor VIII inhibitor166 BU/mL(<1)
Factor IX inhibitor1 BU/mL(<1)
vWF activity>200%(60–170)