Case Report
Spontaneous Epidural Hemorrhage in Sickle Cell Disease, Are They All the Same? A Case Report and Comprehensive Review of the Literature
| Case report | Year | Age (years) | Sex | Haplotype | Presentation | Identification of EDH after hospitalization | Location of EDH | Subgaleal hemorrhage | Subperiosteal collection | Skull infarction | DIC present | Outcome |
| Current case | 2019 | 19 | Female | HbSS | VOC | 24 hours | R FP | No | No | No (CT/IO) | Yes | Died | Komarla et al. [17] | 2018 | 18 | Female | Unspecified | VOC | 24 hours | R parietal | No | No | Yes (MRI) | N/S | Survived | 17 | Male | Unspecified | Headache | POA | Bifrontal | Yes | Yes | Yes (MRI) | N/S | Survived | Banerjee et al. [18] | 2018 | Teenage | Male | HbSS | VOC | 6 hours | L frontal | No | No | No (MRI) | Yes | Died | Moyen et al. [19] | 2018 | 13 | Male | HbSS | Seizure | Imaging not performed till day 8 | R FP | No | N/S | No (MRI) | No | Died | Mishra et al. [20] | 2017 | 18 | Male | HbSS | VOC | 120 hours | R parietal | Yes | No | Yes (IO) | No | Survived | Gajjar and Gupta [21] | 2015 | 20 | Male | Unspecified | Headache | POA | L PT | No | No | No (CT) | No | Survived | Hettige et al. [22] | 2015 | 7 | Female | HbSS | Coma | POA | B/L parietal | No | No | No (CT/IO) | Yes | Died | Yogarajah at al. [23] | 2015 | 19 | Male | HbSC | VOC | 24 hours | R PT | No | No | No (CT/IO) | No | Survived | N’dri Oka et al. [24] | 2015 | 19 | Male | HbSC | Headache | POA | Occipital | Yes | No | No (CT) | No | Survived | Ilhan et al. [25] | 2014 | 15 | Male | HbSS | Headache | POA | Right frontal | Yes | No | Yes (MRI) | No | Survived | Serarslan et al. [26] | 2014 | 19 | Female | HbSS | Headache | POA | L FP | No | No | No (CT/IO) | No | Survived | Page et al. [27] | 2014 | 20 | Male | HbSS | VOC | 48 hours | L frontal | Yes | No | Yes (MRI) | No | Survived | 7 | Female | HbSS | Coma | POA | R temporal | No | | Yes (MRI) | No | Survived | Babatola et al. [28] | 2012 | 18 | Male | HbSS | Headache | POA | R Frontal | No | No | No (CT/IO) | No | Survived | Bolke and Scherer [29] | 2012 | 19 | Male | Unspecified | VOC | 72 hours | L frontal | No | No | No (CT/IO) | No | Died | Patra et al. [30] | 2012 | 13 | Male | Unspecified | Headache | POA | B/L parietal | No | No | No (CT) | No | Survived | Arends et al. [31] | 2011 | 19 | Male | HbSC | Headache | POA | R parietal | No | No | Yes (MRI) | No | Survived | Sangle et al. [32] | 2011 | 15 | Male | Unspecified | Headache | 12 hours | Bifrontal | No | No | No (MRI) | No | Died | Azhar [33] | 2010 | 12 | Male | HbSD | VOC | 24 hours | L frontal | No | No | N/S (CT) | N/S | Survived | Dahdaleh et al. [34] | 2009 | 18 | Male | Unspecified | VOC | 12 hours | B/L FP | Yes | No | No (CT/IO) | No | Survived | Kotb et al. [35] | 2006 | 10 | Male | Unspecified | Headache | N/S | Bifrontal | Yes | No | Yes (MRI) | N/S | Survived | Kalala Okito et al. [36] | 2004 | 2 | Male | HbSS | Coma | POA | R FT | No | No | N/S (IO) | N/S | Died | 12 | Male | HbSS | VOC | N/S | L parietal | No | No | Yes (X-ray) | No | Survived | Ganesh et al. [37] | 2001 | 11 | Male | HbSS | Proptosis | POA | Bifrontal | Yes | No | Yes (BS) | N/S | Survived | Naran and Fontana [38] | 2001 | 16 | Male | Unspecified | Headache | ? POA | R Frontal | No | No | Yes (MRI/BS) | No | Survived | Cabon et al. [39] | 1997 | 14 | Female | HbSS | Unknown | Unknown | Bifrontal | Unknown | Unknown | Yes | Unknown | Unknown | Resar et al. [40] | 1996 | 14 | Male | HbSS | VOC | 48 hours | Left parietal and B/L frontal | Yes | Yes | Yes (MRI/BS) | No | Survived | Tony et al. [41] | 1995 | 35 | Male | Sickle- thalassemia | Proptosis | POA | Left frontal | No | No | Yes (BS) | No | Survived | Karacostas et al. [42] | 1991 | 19 | Male | HbSS | VOC | 48 hours | Left frontal | No | No | No (CT) | No | Survived | Mallouh et al. [43] | 1987 | 13 | Male | HbSS | Eye swelling | POA | Bifrontal | No | No | Yes | N/S | Survived |
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