Case Report

Spontaneous Epidural Hemorrhage in Sickle Cell Disease, Are They All the Same? A Case Report and Comprehensive Review of the Literature

Table 1


Case reportYearAge (years)SexHaplotypePresentationIdentification of EDH after hospitalizationLocation of EDHSubgaleal hemorrhageSubperiosteal collectionSkull infarctionDIC presentOutcome

Current case201919FemaleHbSSVOC24 hoursR FPNoNoNo (CT/IO)YesDied
Komarla et al. [17]201818FemaleUnspecifiedVOC24 hoursR parietalNoNoYes (MRI)N/SSurvived
17MaleUnspecifiedHeadachePOABifrontalYesYesYes (MRI)N/SSurvived
Banerjee et al. [18]2018TeenageMaleHbSSVOC6 hoursL frontalNoNoNo (MRI)YesDied
Moyen et al. [19]201813MaleHbSSSeizureImaging not performed till day 8R FPNoN/SNo (MRI)NoDied
Mishra et al. [20]201718MaleHbSSVOC120 hoursR parietalYesNoYes (IO)NoSurvived
Gajjar and Gupta [21]201520MaleUnspecifiedHeadachePOAL PTNoNoNo (CT)NoSurvived
Hettige et al. [22]20157FemaleHbSSComaPOAB/L parietalNoNoNo (CT/IO)YesDied
Yogarajah at al. [23]201519MaleHbSCVOC24 hoursR PTNoNoNo (CT/IO)NoSurvived
N’dri Oka et al. [24]201519MaleHbSCHeadachePOAOccipitalYesNoNo (CT)NoSurvived
Ilhan et al. [25]201415MaleHbSSHeadachePOARight frontalYesNoYes (MRI)NoSurvived
Serarslan et al. [26]201419FemaleHbSSHeadachePOAL FPNoNoNo (CT/IO)NoSurvived
Page et al. [27]201420MaleHbSSVOC48 hoursL frontalYesNoYes (MRI)NoSurvived
7FemaleHbSSComaPOAR temporalNoYes (MRI)NoSurvived
Babatola et al. [28]201218MaleHbSSHeadachePOAR FrontalNoNoNo (CT/IO)NoSurvived
Bolke and Scherer [29]201219MaleUnspecifiedVOC72 hoursL frontalNoNoNo (CT/IO)NoDied
Patra et al. [30]201213MaleUnspecifiedHeadachePOAB/L parietalNoNoNo (CT)NoSurvived
Arends et al. [31]201119MaleHbSCHeadachePOAR parietalNoNoYes (MRI)NoSurvived
Sangle et al. [32]201115MaleUnspecifiedHeadache12 hoursBifrontalNoNoNo (MRI)NoDied
Azhar [33]201012MaleHbSDVOC24 hoursL frontalNoNoN/S (CT)N/SSurvived
Dahdaleh et al. [34]200918MaleUnspecifiedVOC12 hoursB/L FPYesNoNo (CT/IO)NoSurvived
Kotb et al. [35]200610MaleUnspecifiedHeadacheN/SBifrontalYesNoYes (MRI)N/SSurvived
Kalala Okito et al. [36]20042MaleHbSSComaPOAR FTNoNoN/S (IO)N/SDied
12MaleHbSSVOCN/SL parietalNoNoYes (X-ray)NoSurvived
Ganesh et al. [37]200111MaleHbSSProptosisPOABifrontalYesNoYes (BS)N/SSurvived
Naran and Fontana [38]200116MaleUnspecifiedHeadache? POAR FrontalNoNoYes (MRI/BS)NoSurvived
Cabon et al. [39]199714FemaleHbSSUnknownUnknownBifrontalUnknownUnknownYesUnknownUnknown
Resar et al. [40]199614MaleHbSSVOC48 hoursLeft parietal and B/L frontalYesYesYes (MRI/BS)NoSurvived
Tony et al. [41]199535MaleSickle- thalassemiaProptosisPOALeft frontalNoNoYes (BS)NoSurvived
Karacostas et al. [42]199119MaleHbSSVOC48 hoursLeft frontalNoNoNo (CT)NoSurvived
Mallouh et al. [43]198713MaleHbSSEye swellingPOABifrontalNoNoYesN/SSurvived