Case Report
Atypical Hemolytic Uremic Syndrome following Acute Type A Aortic Dissection
Table 1
Diagnostic tests for TMA-related disease.
| | Parameters | Results | Normal range |
| | Shiga-toxin-producing Escherichia coli infection | | Stool culture | Negative | Negative | | O-157 LPS Ab | Not detected | Not detected |
| | Diagnostic tests for TTP | | ADAMTS-13 activity (%) | 69.1 | 70–120 | | Anti-ADAMTS-13 antibody (BU/mL) | <0.5 | <0.5 |
| | Diagnostic tests for secondary TMA | | C3 (mg/dL) | 96 | 65–135 | | C4 (mg/dL) | 11 | 13–35 | | CH50 (IU/ml) | 42.2 | 30–46 | | Direct Coombs test | Negative | Negative | | Indirect Coombs test | Negative | Negative | | Anti-nuclear antibody (titer) | <1 : 20 | <1 : 40 | | PR3-ANCA (IU/ml) | Not detected | <3.5 | | MPO-ANCA (IU/ml) | Not detected | <3.5 | | Lupus anticoagulant | Negative | Negative | | CLβ2GPI (IU/ml) | Not detected | <10 |
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O-157 LPS Ab: O-157 lipopolysaccharide antibody, TTP: thrombocytopenic purpura, ADAMTS-13: a disintegrin-like and metalloproteinase with thrombospondin type 1 motifs 13, PR-3 ANCA: proteinase 3 anti-neutrophil cytoplasmic antibody, MPO-ANCA: myeloperoxidase anti-neutrophil cytoplasmic antibody CLβ2GPI: anti-cardiolipin β2-glycoprotein I complex antibody.
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