Case Report

Refractory Hepatic Hydrothorax: A Rare Complication of Systemic Sclerosis and Presinusoidal Portal Hypertension

Table 1

Cardiac and portal pressure measurements.

Right cardiac catherization (mmHg)
InitialRA 5, PA 31/15 (mean 22)
After albuminRA 13, PA 57/30 (mean 39), PWP 20, CO 5.5 L/min
PFTsDLco 9.33 L, VC 2.75 L
Portal pressure measurements (mmHg)
Initial after albuminFHVP 16, WHVP 17, HVPG 1
Pre-TIPS without albuminFHVP 2, WHVP 4, HVPG 5, PVP 15, PPG 11
Post-TIPSFHVP 5, WHVP 7, HVPG 2, PVP 14, PPG 7

RA: right atrial pressure, PWP: pulmonary wedge pressure, CO: cardiac output, FHVP: free hepatic vein pressure, WHVP: wedge hepatic vein pressure, HVPG: hepatic vein pressure gradient, PVP: direct portal venous pressure measurement, PPG: portal pressure gradient (PVP minus WHVP), PFTs: pulmonary function tests, DLco: diffusion capacity of carbon dioxide, VC: vital capacity, TIPS: transjugular intrahepatic portosystemic shunt.