Case Report

Fibrolamellar Hepatocellular Carcinoma and Noncirrhotic Hyperammonemic Encephalopathy

Table 2

Urea cycle metabolites.

LaboratoryPatient’s valueNormal value

Pyruvic acid0.11 mmol/L0.03 – 0.12 mmol/L

L-lactate lactic acid1.23 mmol/L0.5 – 2.2 mmol/L

Lactate/pyruvate ratio11.180- 25

Phosphoserine11 umol/L1 to 17 umol/L

Taurine47 umol/L11- 202 umol/L

Phosphoethanolamine0 umol/L0 – 189 umol/L

Aspartic acid7 umol/L0- 31 umol/L

Threonine33 umol/L45 – 194 umol/L

Serine44 umol/L73 – 154 umol/L

Asparagine46 umol/L32 – 98 umol/L

Glutamic acid141 umol/L34 – 177 umol/L

Glutamine399 umol/L204 – 1101 umol/L

Glycine95 umol/L94 – 553 umol/L

Alanine145 umol/L161 – 535 umol/L

Citrulline9 umol/L1 – 33 umol/L

Ornithine68 umol/L16 – 129 umol/L

Arginine18 umol/L13 – 128 umol/L

Lysine63 umol/L35 – 220 umol/L

Anti-citrulline antibodies< 7 IU/ml0 – 16 IU/ml

Urinary orotic acid2.3 mmol/mmol creatinine0.4 – 5.1 mmol/creatinine