Case Report
Fibrolamellar Hepatocellular Carcinoma and Noncirrhotic Hyperammonemic Encephalopathy
| Laboratory | Patient’s value | Normal value |
| Pyruvic acid | 0.11 mmol/L | 0.03 – 0.12 mmol/L |
| L-lactate lactic acid | 1.23 mmol/L | 0.5 – 2.2 mmol/L |
| Lactate/pyruvate ratio | 11.18 | 0- 25 |
| Phosphoserine | 11 umol/L | 1 to 17 umol/L |
| Taurine | 47 umol/L | 11- 202 umol/L |
| Phosphoethanolamine | 0 umol/L | 0 – 189 umol/L |
| Aspartic acid | 7 umol/L | 0- 31 umol/L |
| Threonine | 33 umol/L | 45 – 194 umol/L |
| Serine | 44 umol/L | 73 – 154 umol/L |
| Asparagine | 46 umol/L | 32 – 98 umol/L |
| Glutamic acid | 141 umol/L | 34 – 177 umol/L |
| Glutamine | 399 umol/L | 204 – 1101 umol/L |
| Glycine | 95 umol/L | 94 – 553 umol/L |
| Alanine | 145 umol/L | 161 – 535 umol/L |
| Citrulline | 9 umol/L | 1 – 33 umol/L |
| Ornithine | 68 umol/L | 16 – 129 umol/L |
| Arginine | 18 umol/L | 13 – 128 umol/L |
| Lysine | 63 umol/L | 35 – 220 umol/L |
| Anti-citrulline antibodies | < 7 IU/ml | 0 – 16 IU/ml |
| Urinary orotic acid | 2.3 mmol/mmol creatinine | 0.4 – 5.1 mmol/creatinine |
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