Case Report

IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin Tumor

Table 1

The literature review of reported IgG4-related hepatic IPTs to date.

AuthorYearAgeSexTumor number/locationBiopsyBiopsy methodResectionInitial diagnostic impressionSerum IgG4

Adachi K [14]201760M1/Segment 3NYHepatic cancerElevated
Adachi Y [15]202080sF1YUnspecifiedNHepatic IPTElevated
Ahn KS [9]201258M1YRecurrence of Klatskin tumor
60M1YMalignancy
76M2NHepatic IPT
52M1NHepatic IPT
Buchter M [16]201858MYUnspecifiedNHodgkin’s lymphoma2528
Chia JS [17]202053MNY
Chung JW [18]201967M1YPercutaneousYAbscess, cancer2215
Fujisaki H [19]201675F1/Segment 7NYHepatic IPTSerum normal, bx elevated
Hamano A [6]202071M1/Segment 3YPercutaneousNHepatic cholangiocarcinoma180
Hastir D [20]201350F1/Segment 5NYHepatocellular carcinoma
Horiguchi S [21]201276M1/Segment 2YLaparoscopicN819
Itazaki Y [2]202175F1YCholangiocarcinoma
Kanno a [22]200548MNYLiver metastasis from cholangiocarcinoma2150
Kataoka K [23]201779MYUnspecifiedNElevated
Kim F [24]201158M1/Segment 4YPercutaneousN1470
Lee YS [25]201359M1/Segment 5YPercutaneousNInoperable gallbladder cancer75
Legkiy O [26]201960M2/Segment 2 & 6YPercutaneousY19.1
Matsuo Y [27]201474M1/Segment 8NYLiver metastasis from GIST
Miyajima S [28]201750F1YUnspecifiedNCholangiocarcinoma241
Mulki R [29]201550M2NYAbscess with impending rupture>182
Naitoh I [30]200977M1/Segment 3NYIntrahepatic cholangitis231
Patel H [10]201848M1YUnspecifiedN2228
Shibata M [4]201672M1/Segment 7YPercutaneousN137
Uchida K [31]200754M1/Segment 4YUnspecifiedNPancreatic cancer with liver metastasis213
Vadi S [32]201854M1/Gallbladder fossaYUnspecifiedN356
Wang M [33]202078M1/Segment 4NYCholangiocarcinoma
Yang L [34]201560M1/Segment 3YUnspecifiedN1590
Yueh HZ [35]202147MMultipleYPercutaneousNMetastatic cancer1786
Zen Y(16 cases) [36]1990–2005Avg 67 (56–82)11M 5FNY(All resected)Hilar cholangiocarcinoma (8), intrahepatic cholangiocarcinoma (5), malignant hepatic tumor, undetermined origin (2), metastatic carcinoma (1)