Case Report

Hereditary Angioedema Type II: First Presentation in Adulthood with Recurrent Severe Abdominal Pain

Table 1

Complement studies.

ā€‰Ref. Range12/08/201615/09/20163/11/201629/04/ 2018

C1 Esterase Inhibitor function41->67%2293529
C1 Esterase Inhibitor serum level210 - 390 mg/LNot done450610780
C49 - 36 mg/dL2356
C390 - 180 mg/dL114104140134
Serum C1q303 - 610 nmol/L--377-